Back احمضاض الدم العضوي Arabic Органична анемия Bulgarian Organoazidopathie German ارگانیک اسیدوری Persian Acidosi organiche Italian Kwasice organiczne Polish
| Organic acidemia | |
|---|---|
| Other names | Organic aciduria, Organic acid disorder |
Organic acidemia is a term used to classify a group of metabolic disorders which disrupt normal amino acid metabolism, particularly branched-chain amino acids, causing a buildup of acids which are usually not present.[1]
The branched-chain amino acids include isoleucine, leucine and valine.[1] Organic acids refer to the amino acids and certain odd-chained fatty acids which are affected by these disorders.
The four main types of organic acidemia are: methylmalonic acidemia, propionic acidemia, isovaleric acidemia, and maple syrup urine disease.[1]